Data Management And Sharing System of China National Clinical Research Center for Neurological Diseases

《国家中心数据管理与共享系统操作说明书 —— 研究者部分》

Clinical Perspective on Dysplastic Gangliocytoma of the Cerebellum (Lhermitte-Duclos Disease)

First author：Ma Jun

Corresponding author：Jia Wang

Central nervous system (CNS) Dysplastic gangliocyt

essential_information

  • Person in charge：Ma Jun
  • Data Sources： OTHERS
  • Number of papers：OTHERS20190745
  • Published time：2019-02-01

2019-02-01

Published articles

Journal：World Neurosurg

Publication type: Case Report

IF(IF): 2.104

PMID: 30366139 Link To Pubmed Full text Download

Background And Purpose

Method

Here we introduced a newly diagnosed adult case with intratumoral hemorrhage. Then we reviewed 18 cases diagnosed in our institute, including 12 adults and 6 children.

Conclusion

Preoperative diagnosis based on magnetic resonance imaging is 50% in adults and 16.7% in pediatrics. Diagnostic tiger stripes are not always seen in pediatric cases. The prognosis of the disease is good if total resection can be achieved. Further examinations for PTEN mutation and other comorbidities are recommended.

Main results

Preoperative diagnosis based on magnetic resonance imaging is 50% in adults and 16.7% in pediatrics. Diagnostic tiger stripes are not always seen in pediatric cases. The prognosis of the disease is good if total resection can be achieved. Further examinations for PTEN mutation and other comorbidities are recommended.